Idiopathic pulmonary fibrosis ( IPF ) , is a disease of scarring of lungs which mostly affects one-time age and middle aged adults , without a known cause . Since the exact case of Idiopathic pulmonic fibrosis ( IPF ) is still unknown , it is seen that genetic science can play a role in being a staunch agent . When multiple member of the same family have idiopathic pneumonic fibrosis , the disease is also known as hereditary Idiopathic pulmonary fibrosis ( IPF ) .
Causes of Idiopathic Pulmonary Fibrosis
As stated above , the precise case of idiopathic pulmonic fibrosis is still unknown there are sure weather relate to this condition :
Another related to precondition is hypersensitivity pneumonitis in which idiopathic pulmonary fibrosis can develop . Idiopathic pulmonic fibrosis ( IPF ) results from inhaling any debris contaminate with any bacterium , fungus or any type of animal product .
Also in some the great unwashed , continuing pneumonic fibrosis develops without any known cause . Many mass with Idiopathic pulmonary fibrosis ( IPF ) do not reply to the various medical therapies . Whereas in some patients with nonspecific interstitial pneumonitis ( NSIP ) , respond to the immune suppressive therapy .
Stages of Idiopathic Pulmonary Fibrosis
Idiopathic pneumonic fibrosis has been very loosely staged by medical experts and the disease varies from balmy , temperate , stark or early advanced disease . stage of idiopathic pulmonary fibrosis are incur on the basis of pulmonic affair exam .
Here are two propose staging systems as given :
Simply say , on the cornerstone of various parameter , the level of idiopathic pneumonic fibrosis are judged . base on the pulmonary function test the level are graded as
Further stages of idiopathic pneumonic fibrosis also depended on the results of six minute walking test and other innovative investigations and CAT scan .
Signs and Symptoms of Idiopathic Pulmonary Fibrosis
unremarkably the signs and symptoms of idiopathic pulmonary fibrosis have a very slow and relentless progression in the human body . Here are some signs and symptom of idiopathic pulmonary fibrosis :
Treatment of Idiopathic Pulmonary Fibrosis
Treatment of idiopathic pulmonic fibrosis usually depends on any related to condition that can be treat . So far no effective or perfect treatment for Idiopathic pneumonic fibrosis ( IPF ) has been develop yet since scarring once developed is lasting . The treatment option for Idiopathic pulmonary fibrosis ( IPF ) are very limited .
A promising treatment of idiopathic pulmonic fibrosis is lung transplantation , the only therapeutic pick available till now . And at times , lung diagnosing becomes difficult even when the tissue paper biopsy has been reviewed by the pathologists . However , inquiry trial are being done so by using dissimilar sort of drugs , which help in reduce the on-going scarring in the lungs .
Newer drug are being researched and are tried , which may bring in some Bob Hope in the treatment of idiopathic pneumonic fibrosis . So far the results from such newer drugs obtained have also shown dense progression of scarring of lung and it has also brought some minor change in the lung tests done . But unfortunately , few of the side effects due to consumption of these medications have forced affected role to cease their inlet .
As a part of the treatment of lung fibrosis corticoid and other drugs that suppress the immune system of rules of the body , may be prescribed to slow the procession of fibrosis . But the fact is these type of drugs do not help in the idiopathic pulmonary fibrosis . Similar palliative intervention and medications to hold the symptoms may be prescribed .
It must also be carry in the mind that the toxic level and side effects of the medications can be very dangerous too . Some of the treatment used to treat such conditions include :
Also , the anti - inflammatory medicine colchicine also is used ; but with a very circumscribed form of succeeder . Other trials and trial done with other drugs such as Vasco da Gamma interferon and other immune appetite suppressant are play sample for intervention of idiopathic pulmonic fibrosis .
pneumonic artery is a vessel that carry rake from the kernel to the lungs to oxygenize it . Pulmonary fibrosis also keep down the oxygen level in the blood , leading to hypoxia and can also lift pressure in the pneumonic artery of the heart . The shape is pulmonary hypertension and can also pass to failure of the right ventricle of nub . Hence , patients suffering from pneumonic hypertension are also aboard treated with subsidiary oxygen to forestall pulmonary high blood pressure .
Prognosis of Idiopathic Pulmonary Fibrosis
forecast of idiopathic pneumonic fibrosis depends on the point of the disease and the overall health precondition of the person . The prime goal of treatment for Idiopathic pneumonic fibrosis ( IPF)by using the immune suppressing drugs like the corticosteroids is decreasing the inflammation of lung and subsequent scarring in the soundbox . Various response to the treatments are seen . But once the scarring has develop , it becomes permanent . In many cases , Idiopathic pulmonary fibrosis ( IPF ) turn out to be a last sickness and may show a spirit anticipation of around 3 to 5 years after diagnosis .
