What is Moebius Syndrome?
Moebius Syndrome is an super uncommon congenital neurologic condition in which there is impuissance or palsy of the cranial mettle , specially the 6th and the 7th cranial heart . In some cases other cranial nerves may also be touch but those are uncommon .
A child with Moebius Syndrome in whom the cranial cheek 7th is affected will have problem with smiling , lower , lift the supercilium , and closing the lid . If the 6th nerve is touch on in the child then he or she will have problem with turning the optic yesteryear midline .
Some of the other defects associated with Moebius Syndrome are that the pectoralis heftiness may stay underdeveloped and there may be deformities of the limb as well . Moebius Syndrome may be innate but it does not get on as the nipper acquire and hence the deformities and abnormality that the kid may be having at birth do not worsen with time .
The exact cause of Moebius Syndrome is not yet known but it is believed to occur in tyke digest to mothers who may have maltreat recreational drug while pregnant . In some typesetter’s case , Moebius Syndrome tend to occur in families suggesting a genetic connexion to the development of Moebius Syndrome .
What Causes Moebius Syndrome?
As tell , the exact causal agency of Moebius Syndrome is not yet known but mothers who abuse unpaid drug in pregnancy may have a child with Moebius Syndrome . In some fount , it is suggested that a temporary vascular freakishness in the foetus in the initial degree of gestation may also result in development of Moebius Syndrome .
Some female person who use miscarriage medicines like misoprostol may also have a child with Moebius Syndrome . There has been no confirmed cistron defect that has been associate to Moebius Syndrome but sure genes have been identified that may be link up to the development of Moebius Syndrome .
What are the Symptoms of Moebius Syndrome?
The abnormalities present in a child with Moebius Syndrome are quite variable and the severity of the shortage and mental defectiveness also differ from lawsuit to case . The classic presenting feature which has been widely accept as symptom of Moebius Syndrome are
Some of the other symptoms of Moebius Syndrome admit exuberant drooling , strabismus , inability to move the eye sideways , mask like facies , problems with feeding , inadequate sucking abilities , and swallowing trouble .
Children with Moebius Syndrome may have sure deformity as well to admit scant and malformed glossa , small jaw , cleft palate , frequent ear infections , mental defectiveness of the outside pinna with complete absence seizure of the outer portion of the pinna in some fount of Moebius Syndrome .
Treatment for Moebius Syndrome
discourse for Moebius Syndrome is aimed at treating the specific abnormality that the youngster has . This involves a multidisciplinary plan of attack with physicians and surgeons from almost all the strong suit being involve . To treat facial palsy , surgery will be need which may include transferral of muscle or nerves from other region of the body to the brass .
A traditional procedure called as temporalis tendon transfer may be done in some cases of Moebius Syndrome which involves taking the temporalis brawn which help chewing and transfer them to the corners of the oral cavity to facilitate smile . The same type of procedure may be done to meliorate closure of the eyelids as well .
If the paralysis is one-sided meaning that only one part of the face is involve then a surgical operation may be done by taking a healthy centripetal nerve from the commonly the sura and attaching it to branch of the opposite and healthy facial nervus . This cheek regenerates and when it reach the stirred or paralyzed part of the facial nerve then it is link up to the motor nerve .
There is yet another operative procedure for Moebius Syndrome that is being most preferred nowadays in which muscle from the thigh is transferred to the face and connecting the heart that supply blood and nutrients to the masseter muscle to this transferred muscle . This subroutine has prove to be quite effective in improving delivery , facial movements , and improves overall appearance of the child despite suffering from Moebius Syndrome .
strong-arm therapyis extremely vital for children with Moebius Syndrome to deal with the different types of orthopaedic freakishness that they have to dispense with .
Occupational therapy has also been retrieve to be helpful for children with Moebius Syndrome to improve affair of the fingers , hands , groundwork . Speech therapyis required to improve the talking to of the minor .
Strabismus is something which in some cases conk out by on its own with age but in slip if it does not then this condition might be surgically rectify as well . A child with this status may also have to undergo various surgeries to chasten the deformities of the limbs and jaws . These small fry may be provided specialized braces and splints and in some case prosthesis to permit them to move better despite the limb abnormality because of Moebius Syndrome .
