What is Erythromelalgia?
Erythromelalgia is a medical shape where an individual experiences acuteburning pain , pronounced redness ( erythema ) , with gain in the temperature of the skin , particularly of the understructure and hands . Erythromelalgia is also considered a type of neuropathic pain syndrome where the pain in the neck is associated with medical circumstance that touch on the nerves themselves . The small blood line vessels become dilated and congested with descent . Erythromelalgia is commonly bilateral , i.e. dissemble both the sides of the soundbox ; however , it may also be unilateral , i.e. involving only one side of the trunk . The course of action of Erythromelalgia differs greatly from patient to affected role . The onset of the symptom of Erythromelalgia in some patients can be gradual and this condition can rest meek for many age . In some patients , there may be acute or sudden onrush of Erythromelalgia , where it becomes severe over a period of time .
The accurate crusade of erythromelalgia is not know . The case of Erythromelalgia is think to be vasomotor abnormalities or problems with the constriction / narrowing and dilatation / widening of some blood vessels , which get abnormality or to-do in the blood flow rate to the appendage . Erythromelalgia can be a primary or an separated condition or it can fall out secondary to dissimilar underlying medical atmospheric condition . The causal agent of primary erythromelalgia is not hump and it can occur randomly or can be familial indicate an autosomal dominant inheritance .
Types of Erythromelalgia
Erythromelalgia is classified into elemental erythromelalgia and secondary erythromelalgia . Another categorisation is early - onset erythromelalgia and late - onset erythromelalgia .
Causes of Erythromelalgia
The precise cause of erythromelalgia is not known in bulk of the cases . Primary erythromelalgia often develops spontaneously without any related underlying disease . This eccentric of erythromelalgia is also bring up to as ‘ idiopathic erythromelalgia ’ . The causal agent of secondary erythromelalgia is aesculapian conditions , such as neurological diseases ( peripheral neuropathy , multiple sclerosis ) , autoimmune disease ( diabetes mellitus , lupus ) and more commonly myeloproliferative disorder where there is excessive yield of cells by the bone marrow , e.g. polycythemia vera , essential thrombocythemia . Patient experiences erythromelalgia before the myeloproliferative disorder come out in majority of the case .
Patients having other - onset erythromelalgia will develop it before they reach 25 years of age . Even though former - onset erythromelalgia is of unknown origin in majority of the patient , in some case , it can be traced back through many generations of the family . This is cerebrate to pass off due to genetical sport . Late - onset erythromelalgia tends to germinate in individuals who are around 40 to 60 year of age and it presents as chief erythromelalgia in more than one-half of the patient role .
Some of the Potential Causes of Erythromelalgia are :
Signs & Symptoms of Erythromelalgia
Diagnosis of Erythromelalgia
Investigations need to be done to identify the underlying causes in all the unexampled compositor’s case of Erythromelalgia . This condition can also be an other sign of thrombocythemia or polycythemia where the symptom appear before the diagnosing is made . If the cause of Erythromelalgia is myeloproliferative disorders , then patient role can experience dramatic easement with the habit of aspirin . This is a utilitarian aid in diagnosis .
probationary diagnosis of Erythromelalgia can be made based on the symptoms . Immersion of the affected part in blistering piddle for about 20 to 30 minutes can touch off an attack and helps in confirming the diagnosis . When no know underlying cause has been found , then the erythromelalgia is considered primary .
Treatment for Erythromelalgia
If the underlying causal agency is found in secondary erythromelalgia , then it must be cover . treat the symptoms of primary erythromelalgia , as well as subaltern erythromelalgia comprises of materialistic measures , drug therapy and surgical interposition .
Different patients respond differently to drug therapy . There is no prove single therapy which is known to be systematically effective in treating Erythromelalgia . In some casing , patients may have unwritten remissions also .
Surgical Treatment in Erythromelalgia
If the above discussion measures do not provide easement then surgery may be needed to treat Erythromelalgia . operative sympathectomy is a procedure where the sympathetic nerve fibers are selectively cut . In this surgical subroutine for Erythromelalgia , the nervus ending which channelise the pain signals from the hand and feet are cut . This surgery carries serious risk of infection ; however , this procedure is more beneficial in affected role whose tone of life has been severely affected due to erythromelalgia .
Diet in Erythromelalgia
Diet play an important role in handle and managing erythromelalgia . food which are fertile in vitamin B should be consumed , as they help in boost the immune system along with providing relief from symptoms of erythromelalgia . dieting which should be follow in erythromelalgia should contain of the trace foods :
Lifestyle Modifications & Herbal Remedies for Erythromelalgia
The following alteration in the patient role ’s lifestyle help in bringing relief in erythromelalgia and include :
