Poland syndrome is a wellness circumstance in which the muscles face on one side of the body are either missing or underdeveloped since birth . This result in abnormal geological formation of shoulder , breast , arm and bridge player . The extent of severity and contortion change among the individuals get from Poland syndrome .
What is Poland Syndrome?
The chest is composed of two form of muscles which are foretell pectoralis minor and pectoralis major . The pectoralis tyke is a triangular muscle which covers the upperchest rampart , while pectoralis major is a enceinte muscle with fan like structure which covers the front region the dresser and almost the full upper breast .
In case of Poland syndrome , the stirred soul does not possess pectoralis minor as well as the breast osseous tissue part of pectoralis major , in one side of the torso . Though , this condition is uncommon but associated complication can be severe in case of certain abnormalities .
Characteristic Features of Poland Syndrome
The feature of speech of Poland syndrome may change from individual to individual reckon on the severity of the condition . Thus , the features can be categorise into three categories namely common , moderate and rare . The follow are : –
In rare cases both sides of the body may be affected by Poland syndrome .
Epidemiology of Poland Syndrome
Poland syndrome is know to sham one in twenty thousand to one in a million alive births . The incidences of the moved males are double as much as that of females . In case when the severity is soft , the consideration is not diagnose until puberty . Due to the same reasonableness the condition is often underreported and misdiagnosed .
Prognosis of Poland Syndrome
Poland syndrome is known to have an abrupt occurrence rather than familial heritage . In rare cases transmitted inheritance has also been keep . This precondition in certain extreme cases , leads to severe unilateral deformation which may take Reconstruction Period operating room . In cases where the austereness is mild the circumstance can even go unnoticed or unidentified until the individual hits puberty . The circumstance does n’t cause any major problem in the balmy cases , and thus treatment is not required except for cosmetic purpose .
Causes of Poland Syndrome
The causes behind the Poland Syndrome are unknown . It is excogitate that there are certain changes that take place during the 6th week of gestation period which may lead in development of such conditions . The common conjecture is:-
Diagnosis of Poland Syndrome
The diagnosis of Poland Syndrome depends upon the severeness of the condition . It may be diagnosed as early as the fresh - bear period and as late as pubescence . The diagnosing of Poland syndrome is mainly base on clinical evaluation and the associated imaging test like CT Scan , MRI using which the three dimensional and hybridize sectioned range . On the other hand , the X - Ray symptomatic technique can be used to identify the abnormality in thorax , ribs , shoulder , and script and for arm .
Treatment & Management of Poland Syndrome
The Treatment for Poland syndrome is primarily focused on the reconstruction of the abnormal side of the body . The intervention mainly involves operative routine with niggling amount of physiotherapy .
Poland syndrome is a genetic disorder which occurs due to unknown reasons and is characterise by absence seizure or underdevelopment of the bureau muscles and webbed fingers in one side of the torso . Poland Syndrome has an temperamental occurrence and usually impact the correct side of the body . Poland Syndrome is find to be large in males compared to females . Poland Syndrome lead to malformations of breast , limb , hand and breast , the visual aspect which can be prominent as well as mild . In serious cases , affected mortal require surgery for the discipline of the contortion .
