Biliary atresia is a rare liver condition found in child that regard extrahepatic bile duct . It can be inborn ( found at the time of birth ) or acquired ( rule in a couple of weeks after birth ) . Bile duct is responsible for carrying gall from liver to small intestine , which helps in rich metabolism as well as assimilation of fat - soluble vitamins ( vitamin A , D , E and K ) .
Causes and Symptoms of Biliary Atresia
The etiology for biliary atresia still remains ill-defined ; however , it has been postulated that it might develop due to malformations and disruptions in the formation of bile epithelial duct at the sentence of embryogenesis . It has also been linked with chromosomal mental defectiveness , but no specific inherited predisposition has been known . It has also been associated with imbalance in immune organization and viral infections ( cytomegalovirus , rotavirus and reovirus type 3 , Epstein Barr virus , human papillomavirus ) have also been associate with its etiology .
Jaundiceis the most common symptom that is present in all cases of biliary atresia along with dark bleached pee and acholic stools . The shaver also shows signs of weight loss and irritability with progress ofjaundice . Along with the above symptoms , other symptoms may also be present include dilatation of venter due to hepatomegaly or splenomegaly due to portal hypertension . If the disease physical process is not see to it or treated , then it may lead to liver fibrosis and scarring causing cirrhosis and ultimatelyliver unsuccessful person , which leads to death of the infant within 2 - 3 twelvemonth of the onslaught of disease .
Management of Biliary Atresia
The only effectual direction of biliary atresia is Kasai procedure that require removal of the obliterated extrahepatic gall duct and re - found the connection between liver and small intestine by connecting a portion of lowly intestine directly with the liver . This procedure helps find bile drain in about 80 % cases . There is normalization of bilirubin level within 3 months postoperatively , whereas the fecal matter color also come back to normal within first week postoperatively .
What Not To Eat When You Have Biliary Atresia?
What foods to forefend when you have biliary atresia ? Even with the management techniques such as Kasai subprogram , the total amount of bile may not pass on the belittled intestine and there may be health complications related to bile deficiency . This include reduced metabolism of fat , decreased preoccupancy of juicy - soluble vitamins and hypermetabolism . The liver is also gradually damaged due to fibrosis , so liver function is also compromised leading to deficiency in proteins and coagulopathy .
The child becomes malnourished due to insufficiency in nutrients and weight loss pursues . The patients of biliary atresia are usually give a well balanced diet with right nutrients and supplement that combat protein deficiency , productive lack , and fertile - soluble vitamins want including vitamin A , D , E and K. Vitamin A inadequacy leads to dark blindness ; vitamin D deficiency leads to Ca deficiency causing rachitis and osteoporosis ; vitamin eastward want leads to decline in exemption , peripheral neuropathy and ataxia and vitamin K deficiency conduct to hemorrhaging , particularly esophageal varix that is normally see in patients of biliary atresia .
There are certain foods that should be forfend when one has bilious atresia .
In bilious atresia cases , the child is usually deficient in fat due to incomplete metabolism of fat and hence , digestion take to steatorrhea ( excess fat evacuation in ordure ) . Since trunk does not endure and take up most of the avoirdupois , medium chain triglyceride are given in place of other figure of fats . However , all fats should not be replaced by average concatenation triglycerides in ordination to prevent all important fatty pane deficiencies . Therefore , neither medium string triglyceride should be select in excess nor should recollective mountain chain triglycerides be completely eliminate from the dieting . If there is consumption of surplus adipose tissue then it will be excreted in feces .
Overfeeding should be avoided in patient of biliary atresia for decrease risk ofobesityafter liver transplantation . There have been more cases of fleshiness in biliary atresia children due to overfeed in fear of malnutrition .
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